Tetralogy of Fallot

3mo M with GI illness and dehydration and undiagnosed Tetralogy of Fallot. Dehydration worsens right ventricular outflow tract obstruction leading to “Tet Spell” and progressively worsening cyanosis and shock.

Tetralogy of Fallot Case Outline PDF

Tetralogy of Fallot Teaching Debrief Powerpoint

Critical Actions:

1. Supplemental O2

2. Consideration of Tet Spell as etiology of shock and cyanosis

3. Knees to chest position

4. Phenylephrine

5. Sedation to decrease agitation